Anti-FH antibody
Specifications
| Product Cat#: | AB-06-4858 |
| Product type: | Primary antibody |
| Antigen: | FH |
| Immunogen: | Recombinant protein within human FH aa 50-300. |
| Species immunized: | Rabbit |
| Isotype: | IgG |
| Applications: | Western Blot (1:400-1:2000); Immunohistochemistry-Paraffin (1:40-200); Immunocytochemistry (1:40-1:100) |
| Reactivity: | Human, Mouse, Rat |
| Clonality: | Polyclonal |
| Form: | Liquid |
| Buffer: | 1*PBS buffer (pH7.4), 0.2% BSA, 50% Glycerol, 0.05% NaN3. |
| Concentration: | 1 mg/ml |
| Purity: | Immoungen affinity purified. |
| Storage: | Aliquot and freeze at -20°C. Avoid multiple freeze/thaw cycles. |
| Conjugate: | Unconjugated |
| Alternative names: | FH antibody |
| Fumarase antibody | |
| Fumarate hydratase antibody | |
| Fumarate hydratase mitochondrial antibody | |
| Fumarate hydratase, mitochondrial antibody | |
| FUMH_HUMAN antibody | |
| HLRCC antibody | |
| LRCC antibody | |
| MCL antibody | |
| MCUL 1 antibody | |
| MCUL1 antibody | |
| MS709 antibody | |
| Multiple hereditary cutaneous leiomyomata antibody |
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Target information
The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle, or Krebs cycle, and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form, differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion, where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy. [provided by RefSeq, Jul 2008]
Provider
Erpantech Laboratory
